Mohammad Etezad Razavi - Eye Research Center, Mashhad University of Medical Sciences, Mashhad, Iran
Seyed Hossein Ghavami Shahri - Assistant Professor of Ophthalmology Department of Ophthalmology, School of Medicine Khatam Al Anbiya Hospital Mashhad University of Medical Sciences
Farid Shekarchian - Eye Research Center, Mashhad University of Medical Sciences, Mashhad, Iran
Hamid Reza Heidarzadeh - Eye Research Center, Mashhad University of Medical Sciences, Mashhad, Iran
Sepide Hajmohammadi - Department of Pediatrics, Mashhad University of Medical Sciences, Mashhad, Iran

Purpose: This article aimed to report an infant case of congenital neutropenia (CN) with periorbital ecthyma gangrenosum (EG) due to pseudomonas aeruginosa septicemia.Case report: A previously healthy six-month-old male infant with fever, diarrhea, poor feeding, pancytopenia, periorbital swelling, and eyelid ulcers in the left eye was admitted in pediatric intensive care unit (PICU). He had positive blood and eyelid wound cultures for pseudomonas aeruginosa. He was treated with broad spectrum intravenous antipseudomonal antibiotics and debridement of periorbital lesions and discharged after ۱۸ days with a stable condition. Adequate hematologic workup for pancytopenia revealed the diagnosis of CN.Conclusion: There is a possibility that EG be developed in patients with immunodeficiency as preseptal cellulitis with isolated typical lesions, and this should be considered in the treatment.

Ecthyma Gangrenosum, Pseudomonas aeruginosa, Congenital Neutropenia, case report