Gholam Hossain Yaghoobi - Professor of Ophthalmology, Department of Ophthalmology, Valiasr Hospital, Birjand University of Medical Sciences, Birjand, Iran.
Malihe Nikandish - Assistant of Professor, Department of Ophthalmology, Valiasr Hospital, Birjand University of Medical Sciences, Birjand, Iran

We reported the case of a ۹-year-old boy with a complete right blue iris and left brown iris. Other Ophthalmic examinations were normal except for the homonymous symmetrical pattern of nasal retinal hypopigmentation. The case had no systemic finding or positive family history. The present case was unique because the presentation of iris heterochromia did not follow Mendelian law and was not associated with any diseases or syndromes.

Heterochromia iridis, Inheritance pattern, Retinal pigmentation