Management of Intravenous Leiomyomatosis of Uterus with Extension to Heart

Background and Aim : Leiomyoma is a benign smooth muscle tumor. Intra-venous extensions of thesetumors occur due to tumor growth within uterine vein or lymphatic vessels. In rare cases, intracaval andintracardiac extension can also be seen. Clinical suspicion of this disease should become certain by use ofimaging techniques. While the treatment is complete resection of the tumor, one or two-stage surgery canbe planned for patient depending on tumor extension and patient s condition.Methods : In this report, a 52-year-old woman with a rare presentation of uterine leiomyoma will bediscussed. While the tumor was extended toward right atrium, the patient had nonspecific symptoms. Byuse of two-stage surgery, separated laparotomy and cardiopulmonary bypass, the tumor was completelyremoved.Results : Complete removal of tumor can guarantee no recurrence and excellent outcome; however,recurrence is expected in one third of patients with incomplete removal.Conclusion : Complete removal of tumor can guarantee no recurrence and excellent outcome; however,recurrence is expected in one third of patients with incomplete removal.

Keywords:

Cardiopulmonary bypass , leiomyomatosis , laparotomy