Hearing Impairments in Consanguineous Marriage

Consanguineous marriage is strongly favored in many large human populations. In the most parts of south Asia, consanguineous marriage account for ۲۰%  to over ۵۰% of the general population. The effect of consanguinity on hereditary deafness has been well studied and documented. Many authors have suggested that approximately one half  of sensory neural hearing loss in children can be attributed to hereditary causes. This research was carried out in Rehabilitation Deputy of welfare organization of Iran in seven provinces. ۱۳۵۲ infants and preschool aged children participate in this research. The prevalence of SNHL due to consanguineous  marriage in first cousin and second cousin were studied. Consanguinity was found among ۴۵.۷% in first cousin and ۱۷.۲% in second cousin. Hereditary Factors were thought  to be the cause of ۸۶۳(۶۲.۹%) of bilateral SNHL children in this research. The incidence of hereditary hearing impairment is very high in developing countries  compared to developed countries. Prevention is essential to reduce the incidence of genetic hearing loss. Consanguinity should be discouraged and genetic counseling is to be applied at least for those at risk of developing genetic diseases including hearing impairments.

Keywords:

Consanguineous marriage , Hearing impairmens , Sensory-neural hearing loss