Lhermitte – Duclos Disease in a Young Adult: Rare Entity

Lhermitte - Duclos disease also called dysplastic gangliocytoma of cerebellum is an extremely rare cerebellar lesion which share features of both malformation and neoplasm. The usual presentation is of raised intracranial pressure along with cerebellar signs. We report a case of 23 year male who presented with headache & diplopia. MRI was suggestive of the diagnosis. Subtotal excision of the mass along with shunt drainage was performed. Post operative course was uneventful. Histopathological features confirmed the diagnosis.

Keywords:

Lhermitte Duclos Disease , Case Report , India